Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss)
Case Report.
DOI:
https://doi.org/10.31053/1853.0605.v79.n2.32922Keywords:
cardiomyopathy, dilated, churg-strauss syndrome, heart failureAbstract
Eosinophilic granulomatosis with polyangiitis, formerly known as Churg-Strauss Syndrome, is a rare pathology that belongs to the group of diseases characterized by necrotizing vasculitis of small and medium-sized systemic blood vessels. Symptomatic cardiovascular involvement occurs in 27% to 47% of Churg-Strauss cases, being one of the most serious manifestations. The diagnosis is usually confirmed with tissue biopsy showing eosinophil infiltration, but with the recent inclusion of cardiac MRI, we can dispense with it.
Early diagnosis is important because prompt treatment is usually associated with improvement in the condition.
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