Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature

Authors

  • Rene Manuel Palacios Huatuco Clínica Universitaria Reina Fabiola
  • diana alejandra Pantoja Pachajoa Clínica Universitaria Reina Fabiola
  • Agustin Ezequiel Pinsak Clínica Universitaria Reina Fabiola
  • Facundo Ignacio Mandojana Clínica Universitaria Reina Fabiola
  • Alejandro Marcelo Doniquian Clínica Universitaria Reina Fabiola

DOI:

https://doi.org/10.31053/1853.0605.v77.n4.29743

Keywords:

arteriovenous fistula, arteriovenous malformations, abdomen acute, congenital abnormalities

Abstract

Introduction: Congenital renal arteriovenous fistula is an abnormal connection between the arterial and venous system. Since the first case described in 1928 by Varela et al, no more than 200 cases have been published.

Material and Method: A 45-year-old woman consulted for severe abdominal and low-back pain associated with arterial hypertension. The CT scan showed an infrarenal retroperitoneal lesion with invasion of neighboring structures.

Results: During the abdominal exploration, a vascular-looking lesion of 60 x 34 x 41 mm was identified. It was associated with right nephrectomy.

Discussion: The etiology of congenital fistulas remains unknown; it is believed that a congenital arterial aneurysm erodes into an adjacent vein and gradually increases its size. Other authors believe that the fistula exists since birth and gradually increases its size until it causes symptoms.

Conclusion: Congenital arteriovenous fistulas are rare entities, representing less than 25% of all renal arteriovenous malformations.

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Author Biographies

Rene Manuel Palacios Huatuco, Clínica Universitaria Reina Fabiola

Servicio de Cirugía General. Clínica Universitaria Reina Fabiola, Universidad Católica de Córdoba.

diana alejandra Pantoja Pachajoa, Clínica Universitaria Reina Fabiola

Servicio de Cirugía General. Clínica Universitaria Reina Fabiola, Universidad Católica de Córdoba.

Agustin Ezequiel Pinsak, Clínica Universitaria Reina Fabiola

Servicio de Cirugía General. Clínica Universitaria Reina Fabiola, Universidad Católica de Córdoba.

Facundo Ignacio Mandojana, Clínica Universitaria Reina Fabiola

Jefe del sector de Cirugía Oncológica. Clínica Universitaria Reina Fabiola, Universidad Católica de Córdoba.

Alejandro Marcelo Doniquian, Clínica Universitaria Reina Fabiola

Jefe del servicio de Cirugía General. Clínica Universitaria Reina Fabiola, Universidad Católica de Córdoba.

References

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Published

2020-12-19

How to Cite

1.
Palacios Huatuco RM, Pantoja Pachajoa diana alejandra, Pinsak AE, Mandojana FI, Doniquian AM. Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature. Rev Fac Cien Med Univ Nac Cordoba [Internet]. 2020 Dec. 19 [cited 2024 Jul. 17];77(4):356-9. Available from: https://revistas.unc.edu.ar/index.php/med/article/view/29743

Issue

Section

Case Report