Síndrome de Gardner

Abstract

Three patients, sisters of e. 12 and 14 years of age with a diagnosis of Gardner's Syndrome are reported The family history indicated that their mather died of a carcinoma of the intestine at "the age of 30. This Syndrome, which is of dominant autosomic interi tance, can be seen in aur city. with EO heterogeneous hereditary features. Oentists must know the oral cavity characteristics of this disease [odontomas. cementomas, cysts, supernumerary teeth) that accompany ga~trie. intestinal, skeletal and tissular disturbances an of other organs [polyps, osteomas, cysts. adenomas), being intestinal poliposis of the colon the most important .feat~re that becbmes an "Adenocarcinoma", in the third ald fourth decade in a 100% of the cases. Its incidence in our city is real. The proper diagnosis is made when the clinical study is completed and

the dentist may be the first ene to watch this syndrome' s feature in the oral cavity. A proper medica! diagnosis would allow a preventive procedure and a patient's control until the "total surgery of the colon". which ia the appropiate therapeutic procedure. is achieved; although there are controversias as regards the time to be carried out.